Case study: An unusual case of incontinentia pigmenti

Presentation

A female in her mid-twenties attended for an eye check because she had experienced a couple of episodes of transient visual field loss. Each had lasted around 30 minutes, but she had not experienced any associated headache or nausea. The visual disturbance was reported as being located in the temporal field of her right eye.

Medical history

Ophthalmic findings

Vision:

External examination:

Figure 1: Anterior OCT showing of the right (a - top) and left (b - bottom) showing relative thinning of the left cornea (R 521, L 510 microns)